{"id":414,"date":"2015-05-21T13:00:00","date_gmt":"2015-05-21T12:00:00","guid":{"rendered":"http:\/\/lesavoirpartage.org\/new\/2015\/05\/21\/jeudi-21-mai-a-16h30-a-pre-texte-jean-claude-willer-revient-avec-une-intervention-consacree-au-theme-des-maladies-orphelines-a-partir-de-lexemple-du-syndrome-de-linsensibilite-co\/"},"modified":"2016-05-17T14:46:39","modified_gmt":"2016-05-17T13:46:39","slug":"jeudi-21-mai-a-16h30-a-pre-texte-jean-claude-willer-revient-avec-une-intervention-consacree-au-theme-des-maladies-orphelines-a-partir-de-lexemple-du-syndrome-de-linsensibilite-co","status":"publish","type":"post","link":"https:\/\/lesavoirpartage.org\/new\/2015\/05\/21\/jeudi-21-mai-a-16h30-a-pre-texte-jean-claude-willer-revient-avec-une-intervention-consacree-au-theme-des-maladies-orphelines-a-partir-de-lexemple-du-syndrome-de-linsensibilite-co\/","title":{"rendered":"Jeudi 21 MAI, \u00e0 16h30 \u00e0 Pr\u00e9 Texte,  Jean-Claude WILLER, revient avec une intervention consacr\u00e9e au th\u00e8me des maladies orphelines \u00e0 partir de l\u2019exemple du syndrome de l\u2019insensibilit\u00e9 cong\u00e9nitale \u00e0 la douleur."},"content":{"rendered":"<h2><strong>Maladies orphelines\u00a0: les insensibilit\u00e9s cong\u00e9nitales \u00e0 la douleur<\/strong><\/h2>\n<p>Apr\u00e8s une introduction\u00a0: d\u00e9finition des maladies orphelines et maladies rares, je prendrai comme exemple le syndrome d\u2019insensibilit\u00e9 cong\u00e9nitale \u00e0 la douleur.<br \/>\nSyndrome complexe comprenant divers types de pathologies.<br \/>\nPour comprendre les sympt\u00f4mes des cas cliniques que j\u2019exposerai, je ferai un bref rappel sur les m\u00e9canismes p\u00e9riph\u00e9riques de la douleur ainsi qu\u2019un survol rapide (mais essentiel) sur le syst\u00e8me nerveux autonome (v\u00e9g\u00e9tatif) pour aborder ensuite\u00a0 la classification mondialement admise des neuropathies sensitives et autonomes h\u00e9r\u00e9ditaires (NSAH) au travers de quelques cas cliniques de patients que j\u2019ai pu examiner.<br \/>\nNous pourrons ensuite discuter d\u2019une part sur la prise en charge m\u00e9dicale et sociale de ces patients tout au cours de leur vie (de dur\u00e9e variable selon les individus) et d\u2019autre part sur le comportement de ces patients vis-\u00e0-vis de la douleur des autres (empathie\u00a0? or not\u00a0?).<\/p>\n","protected":false},"excerpt":{"rendered":"Maladies orphelines\u00a0: les insensibilit\u00e9s cong\u00e9nitales \u00e0 la douleur Apr\u00e8s une introduction\u00a0: d\u00e9finition des maladies orphelines et maladies rares, je prendrai comme exemple le syndrome d\u2019insensibilit\u00e9 cong\u00e9nitale \u00e0 la douleur. Syndrome complexe comprenant divers types de pathologies. Pour comprendre les sympt\u00f4mes des cas cliniques que j\u2019exposerai, je ferai un bref rappel sur les m\u00e9canismes p\u00e9riph\u00e9riques de la douleur ainsi qu\u2019un survol&nbsp;<a href=\"https:\/\/lesavoirpartage.org\/new\/2015\/05\/21\/jeudi-21-mai-a-16h30-a-pre-texte-jean-claude-willer-revient-avec-une-intervention-consacree-au-theme-des-maladies-orphelines-a-partir-de-lexemple-du-syndrome-de-linsensibilite-co\/\" class=\"read-more\">Lire la suite<\/a>","protected":false},"author":1,"featured_media":415,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_mi_skip_tracking":false,"_monsterinsights_sitenote_active":false,"_monsterinsights_sitenote_note":"","_monsterinsights_sitenote_category":0,"footnotes":""},"categories":[19],"tags":[],"class_list":["post-414","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-medecine","cat-19-id"],"acf":[],"_links":{"self":[{"href":"https:\/\/lesavoirpartage.org\/new\/wp-json\/wp\/v2\/posts\/414","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/lesavoirpartage.org\/new\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/lesavoirpartage.org\/new\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/lesavoirpartage.org\/new\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/lesavoirpartage.org\/new\/wp-json\/wp\/v2\/comments?post=414"}],"version-history":[{"count":3,"href":"https:\/\/lesavoirpartage.org\/new\/wp-json\/wp\/v2\/posts\/414\/revisions"}],"predecessor-version":[{"id":896,"href":"https:\/\/lesavoirpartage.org\/new\/wp-json\/wp\/v2\/posts\/414\/revisions\/896"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/lesavoirpartage.org\/new\/wp-json\/wp\/v2\/media\/415"}],"wp:attachment":[{"href":"https:\/\/lesavoirpartage.org\/new\/wp-json\/wp\/v2\/media?parent=414"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/lesavoirpartage.org\/new\/wp-json\/wp\/v2\/categories?post=414"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/lesavoirpartage.org\/new\/wp-json\/wp\/v2\/tags?post=414"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}